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Brooke-Spiegler Syndrome: a case report

Layegh Pouran; Sistani Nourieh Sharifi; Abadian Mohammad

Volume 10, Issue 2 , 2007, , Pages 157-161

Abstract
  Brooke-Spiegler syndrome is a rare autosomal recessive disease characterized by adnexal neoplasms, particularly trichoepithelioma, cylindroma, and occasionally spiradenoma, which usually develop in second to third decades of life. We report this syndrome in a 16-year-old woman with tumors on face and ...  Read More