ORIGINAL_ARTICLE
Kindler Syndrome: 2 Case Reports from India
Kindler syndrome (KS) is a rare autosomal recessive genodermatosis. We report two cases of KS with classical clinical presentations involving skin and mucus membranes. Clinically, both patients had four major features of KS in the form of acral skin blistering, photosensitivity, progressive poikiloderma, and diffuse cutaneous atrophy. Case 1 had associated features in the form of urethral stenosis, skin fragility and palmoplantar keratoderma with extension of the scaling onto the flexor aspect of the wrist and loss of palmar creases. Case 2 had associated features in form of anal stenosis, oesophageal stenosis, skin fragility and palmoplantar keratoderma with loss of palmar creases. An Interesting finding in our report is that both cases have prominent telengectasia involving face and neck regions.
https://www.iranjd.ir/article_101334_f943bdb403737e87f60a72f615b645bf.pdf
2009-12-01
1
4
acral skin blistering
Photosensitivity
poikiloderma
Kindler syndrome
cutaneous atrophy
Atul
Salodkar
1
AUTHOR
Sanjiv
Choudhary
sanjiv_choudhary26@yahoo.com
2
AUTHOR
Sankha
Koley
skoley@gmail.com
3
AUTHOR
ORIGINAL_ARTICLE
Extensive Fibroepithelial-like Polyps on The Foot of an AIDS Patient Following Radiotherapy for Kaposi's Sarcoma
Fibroepithelial polyps, also named as soft warts, skin tags, or acrochordons, are common benign lesions that may occur on trunk or exterimities. Its association with infectious agents is unclear. Herein, We report a case of extensive fibroepithelial -like polyps on the foot of an AIDS patient following radiotherapy for Kaposi's sarcoma.
https://www.iranjd.ir/article_101335_de28f37a5bcbb9fc9e531eb07a0577ca.pdf
2009-12-01
5
7
fibroepithelial polyp
AIDS
Kaposi sarcoma
radiotherapy
Kassahun
Desalegn Bilcha
1
AUTHOR
Wondemagegn
Enbiale
2
AUTHOR
Tewfik
Kassa
3
AUTHOR
ORIGINAL_ARTICLE
Piebaldism and Vitiligo in Two Brothers
Piebaldism is an autosomal dominant uncommon (<1 in 20,000) congenital pigmentary disorder. Depigmented patches are present since birth. They usually remain unchanged throughout life. Vitiligo is its closest differential diagnosis. We report a unique family in which these two dissimilar depigmentations, i.e. piebaldism and vitiligo (with nevus depigmentosus), were noted in two brothers. To the best of our knowledge, this is the first report of this presentation in the literature.
https://www.iranjd.ir/article_101336_0c55e96cd381c92d18ca516f52f3e803.pdf
2009-12-01
8
11
piebaldism
Vitiligo
depigmentation
Sankha
Koley
skoley@gmail.com
1
AUTHOR
Atul
Salodkar
2
AUTHOR
Vikrant
Saoji
3
AUTHOR
Sanjiv
Choudhary
sanjiv_choudhary26@yahoo.com
4
AUTHOR
ORIGINAL_ARTICLE
Cutaneous Infection by Fusarium Solani in an Addict Man with Active Hepatitis C
We describe a 31-year-old man, a known case of hepatitis C infection for 11 years, who presented with a chronic non-healing large deep ulcer on the dorsum of the right foot for five months. Fusarium solani infection was confirmed by skin biopsy and culture. The biopsy specimen showed an unusually extensive dermal invasion with fungal hyphae. The patient's response to oral itraconazole 100 mg/day for 3 months was excellent. Closed monitoring of liver enzymes was done before and during the treatment course.
https://www.iranjd.ir/article_98529_82a02e53fe1fe51ce2e679b17f19b4a2.pdf
2009-12-01
12
15
Fusarium solani
Hepatitis C
Cutaneous Infection
Ayatolahi
Seyed Amin Mossavi-
1
AUTHOR
Farajzadeh
Saeedeh
2
AUTHOR
Fekri
Ali Reza
3
AUTHOR
Vares
Behrooz
4
AUTHOR
Fekri
Sahba
5
AUTHOR
ORIGINAL_ARTICLE
Colocalization of Lichen Planus and Vitiligo: Challenging the Universality of Current Theories
Vitiligo and Lichen Planus, two common dermatologic disorders, are expected to coexist. This leads to diverse theories regarding their immunopathogenesis linkage. In this case, we report a twenty-year-old man suffering from simultaneous lichen planus and vitiligo which were both generalized at the time of observation and also concomitant throughout their entire course of progression. Lichen Planus papules were located on sun-exposed areas and non sun-exposed areas; both on vitiligenous areas and non-vitiligenous areas diminishing current theories about the association of the two diseases. Since we did not have the patient’s consent to perform a series of biopsies, we were unable to evaluate dermatopathology of the two diseases at different sites in regard to sun exposure. Further extensive researches on larger scales seem warranted to propose any kind of theory regarding their interconnection.
https://www.iranjd.ir/article_98528_4d53a57631a27fcea748644d1c040476.pdf
2009-12-01
16
18
Lichen Planus
Vitiligo
colocalization
Concomitant
Hefazi
Mahyar T
1
AUTHOR
Moslehi
Homayon
2
AUTHOR
Ehsani
Amir H
3
AUTHOR
Ostadrahimi
Nima
4
AUTHOR
ORIGINAL_ARTICLE
No Association between Gadolinium-Based Contrast Agents and Development of Nephrogenic Systemic Fibrosis: a Case Study
Nephrogenic systemic fibrosis (NSF), previously known as nephrogenic fibrosing dermopathy, is an emerging systemic fibrosing disorder that develops in the setting of renal insufficiency. Nephrogenic fibrosing dermopathy (NFD) is a fibrosing condition of the skin which shows an increased number of dendritic cells, fibroblasts and thickened collagen fibers resembling scleromyxedema. It is characterized by indurated plaques mainly on the extremities and the absence of paraproteinemia. Although the exact causes of NSF have not been established, evidence suggests an association between gadoliniumbased contrast agents and development of nephrogenic systemic fibrosis. We report a patient who was under dialysis and developed NSF but she never did MRI.
https://www.iranjd.ir/article_101338_7e4dddd9b1ebf1819ae6ba09655c2234.pdf
2009-12-01
19
22
nephrogenic systemic fibrosis
nephrogenic fibrosing dermopathy
MRI
Gadolinium
Bahareh
Malekafzali
1
AUTHOR
Saeed
Pirozi
2
AUTHOR
Vahid R
Yassaee
3
AUTHOR
ORIGINAL_ARTICLE
A Case of Giant Sebaceoma
Sebaceoma is a benign tumor with sebaceous differentiation. It usually presents as a yellowish papule or nodule on the face and scalp. This is a report of a 27-year-old-woman who presented with a giant, 6cm×4.5 cm exophytic tumor on her head. Clinically, we considered several diseases; however, the histological and immunohistochemical features matched those of sebaceoma. The lesion was excised and the defect was repaired by a split-thickness graft.
https://www.iranjd.ir/article_101339_255afe6cb2be273ef8b4d33ddf9fb969.pdf
2009-12-01
23
24
sebaceoma
scalp
sebaceous differentiation
Fatemeh
Mohaghegh
f.mohaghegh@med.mui.ac.ir
1
AUTHOR
Ali
Asilian
afrashteh.mohammad@yahoo.com
2
AUTHOR
Soheila
Taheri
3
AUTHOR
Parvin
Rajabi
4
AUTHOR
ORIGINAL_ARTICLE
Erosive Pressure Dermatitis Associated with Cardiac Pacemaker
Erosive dermatitis is a skin reaction associated with implantable cardiac devices (ie, pacemakers and cardioverter defibrillators). We report a 65-year-old man with a history of several cerebrovascular attacks who developed an erythematous crusted erosive patch over the pacemaker site after implantation of two subsequent pacemakers. We suggest that physical irritation may be a trigger factor for both pacemakers and changing the type of pacemaker is not important in some cases.
https://www.iranjd.ir/article_101340_d9d0cddfbb3f7b629aa6f1e7ef17da9d.pdf
2009-12-01
25
26
PACEMAKER
Erosion
pacemaker dermatitis
Hayedeh
Ghaninejadi
1
AUTHOR
Soheil
Fateh
sfateh@razi.tums.ac.ir
2
AUTHOR
Roghie
Shamsoddini
3
AUTHOR
Farshad
Farshidfar
4
AUTHOR
ORIGINAL_ARTICLE
A Case of Lipomembranous Panniculitis Associated with Rheumatoid Arthritis
Lipomembranous panniculitis is a special type of fat necrosis which has been associated with several clinical conditions, mainly chronic venous insufficiency and connective tissue disorders such as lupus profundus, morphea, systemic sclerosis, and dermatomyositis .We report a 50 yearold woman with known rheumatoid arthritis who presented with a painful indurated erythematous plaque on her right leg. Histologic examination demonstrated cystic areas of fat necrosis lined by wavy eosinophilic hyaline membrane with convoluted projections of the membrane into the cysts. This finding is diagnostic of lipomembranous panniculitis. To our knowledge, this is the first report on lipomembranous panniculitis associated with rheumatoid arthritis.
https://www.iranjd.ir/article_101342_b87977b9e44e423f791048ee0e7efdaf.pdf
2009-12-01
27
29
panniculitis
Rheumatoid arthritis
lipomembranous panniculitis
Zahra
Asadi-Kani
sbmusrc@yahoo.com
1
AUTHOR
Hamideh
Moravvej
sbmusrc@hotmail.com
2
AUTHOR
Mehdi
Gaisari
3
AUTHOR
Sima
Kavand
4
AUTHOR
Marjan
Saeedi
marjan406@yahoo.com
5
AUTHOR
ORIGINAL_ARTICLE
An Unusual Form of Tinea Versicolor: A Case Report
Tinea versicolor is caused by Malassezia furfur and presents as hypo or hyper-pigmented coalescing scaly macules on the trunk and upper arms. Sites of predilection are the sternal region and the sides of the chest, the abdomen, back, pubis, neck, and intertriginous areas. We report a case of tinea versicolor with a reticulated pattern on acral sites.
https://www.iranjd.ir/article_101343_ecab7cd32586e283a576d5b7872e4787.pdf
2009-12-01
30
31
acral
Tinea versicolor
reticulate
Ali Akbar
Akaberi
akaberi44@yahoo.com
1
AUTHOR
Seyed Saeed
Amini
2
AUTHOR
Hosein
Hajihosseini
3
AUTHOR