Epidermolysis Bullosa Puriginosa: Report of a Case
Simin Shamsi Meymandi, Shahriar Dabiri, Hamidreza Shafiei
Epidermolysis Bullosa Puriginosa is a genetic mechanobullous disease characterized by pruritus, lichenified or nodular prurigo-like lesions, occasional trauma-induced blistering, excoriations, milia, nail dystrophy and albopapuloid lesions that appear at birth or later. Scarring and prurigo are most prominent on the shins. Herein, we report a case with a history of blisters since childhood followed by intensely pruritic lesions predominantly on the shins and dystrophy of the toenails, milia, excoriations and diffuse post-lesional hyper and hypopigmentation.
Keywords: dystrophic epidermolysis bullosa puriginosa, pruritis, dermal–epidermal junction
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