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Bullous ichthyosiform erythroderma

Siavash Mohammadzadeh Shanehsaz; Roshan Bittar; Abdollah Anis; Silva Ishkhanian

Volume 16, Issue 3 , 2013, , Pages 112-115

Abstract
  Bullous ichthyosiform erythroderma (BIE) is a rare disorder of keratinization (mutations in either keratin 1 or 10). It typically presents with fragile skin, which gives way to gradual evolutionof hyperkeratosis. Flaccid blisters, peeling, and superficial erosions at sites of minor trauma ...  Read More