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Papillon-Lefevre syndrome: A report of two cases in a family

Ameneh Yazdanfar; Kamran Kaveh

Volume 9, suppl.1 , 2006, , Pages 1-1

Abstract
  Palmoplantar keratodermas are a heterogenous group of diseases, one of them is Papillon-Lefevre Syndrome (PLS). This rare disease is inherited as autosomal recessive and characterized by focal hyperkeratotic plaques on elbows and knees, severe periodontal disease resulting in premature loss of teeth. ...  Read More